Pancreatic somatostatinoma with obscure inhibitory syndrome and mixed pathological pattern |
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| Authors: | Bo Zhang Qiu-ping Xie Shun-liang Gao Yan-biao Fu and Yu-lian Wu |
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| Institution: | (1) Department of General Surgery, Ancona University Hospital, Ancona, Italy;(2) Department of General Surgery, Ancona University Hospital, Via Conca, 60020 Torrette, Ancona, Italy |
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| Abstract: | Somatostatinoma is a very rare neuroendocrine tumor that originates from D cells and accounts for less than 1% of all gastrointestinal
endocrine tumors. The duodenum is the most frequent site for this tumor, followed by the pancreas. We here describe a 46-year-old
Chinese woman who developed pancreatic somatostatinoma presenting with the characteristic “inhibitory” syndrome, but the symptoms
were obscure and seemingly uncorrelated. This case is also unique for its large tumor size and mixed pathological pattern.
Distal pancreatectomy was performed, and the patient has remained well since operation. As the syndromes of somatostatinoma
may be obscure and atypical, clinicians should review all clinical findings to obtain an accurate diagnosis. Aggressive surgery
is preferred to improve the survival. |
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| Keywords: | Neuroendocrine tumor Somatostatinoma Somatostatinoma syndrome Pancreatic hormone-producing tumor Pancreatectomy |
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